Pancreatitis is an earmark of FCS

Published 4:06 am Friday, November 16, 2018

DEAR DR. ROACH: Recently I was diagnosed with FCS (familial chylomicronemia syndrome) by my primary physician. I have extremely high triglycerides and Type 2 diabetes. I have brought my A1C from 10 percent to 6 percent, as well as lost 40 pounds and completely changed my way of eating. I also walk.

Despite this, I have numerous bouts of acute pancreatitis every year. I am hospitalized at least every three months. I am extremely discouraged. During my last bout, my triglycerides were 10,000. Currently they are 1,200. Is there any hope of relief? — T.R.

ANSWER: Familial chylomicronemia syndrome, also called Type 1a hyperlipoproteinemia, is a very rare disorder of fat metabolism caused by the loss of the enzyme lipoprotein lipase, normally made in the pancreas.

The only effective therapy available right now is a diet that is very low in fat, with almost no simple sugars or alcohol.

You have done extremely well in dropping your triglycerides by 90 percent, and reduced your risk of diabetic complications probably by 75 percent, but I understand you are still frustrated with persistent bouts of pancreatitis.



You can find out more about this condition at numerous sites, including https://tinyurl.com/chylosyndrome.